- esp. Turkey
- Iraq, Iran, Arabia, China, Korea, Japan
- Usually presents 20-40 yrs. old
- Painful
- Outbreaks lasting 1-3 weeks, frequent recurrences
- Knees, ankles, wrists
- Usually during ulcer flares
- Acneiform pustules, erythema nodosum, others
- Oral ulcers ≥3 times/yr, PLUS 2 of Following:
- Genital ulcers, idiopathic, recurrent
- Uveitis (Dx’d by slit lamp)
- Skin lesions
- Pathergy: Insert 20 g needle obliquely 5 mm into forearm → >2 mm papule at 24-48 hrs.
- Uveitis [can cause blindness]
- CNS lesions
- Thromboses & vasculitis
See posting Monoarticular / Oligoarticular Arthritis.